E78.1 Pure hyperglyceridemia

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Pure hyperglyceridemia

E78.1BillableFY 2026Chapter 4

Pure hyperglyceridemia

Pure hyperglyceridemia Elevated fasting triglycerides; Endogenous hyperglyceridemia; Fredrickson's hyperlipoproteinemia, type IV; Hyperlipidemia, group B; Hyperprebetalipoproteinemia; Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia

Code classification

4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E78.1Current code

Related terminologies

ORPHA identifiers (rare diseases)

This ICD-10 code maps to the following rare disease(s) in the Orphanet nomenclature:

ORPHA CodeDisease Name
ORPHA:413NON RARE IN EUROPE: Hyperlipoproteinemia type 4

Data from Orphadata (CC BY 4.0). orpha.net

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