E78.1 Pure hyperglyceridemia
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Pure hyperglyceridemia
Pure hyperglyceridemia
Pure hyperglyceridemia Elevated fasting triglycerides; Endogenous hyperglyceridemia; Fredrickson's hyperlipoproteinemia, type IV; Hyperlipidemia, group B; Hyperprebetalipoproteinemia; Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
Code classification
Related terminologies
ORPHA identifiers (rare diseases)
This ICD-10 code maps to the following rare disease(s) in the Orphanet nomenclature:
- 1
| ORPHA Code | Disease Name |
|---|---|
| ORPHA:413 | NON RARE IN EUROPE: Hyperlipoproteinemia type 4 |
Data from Orphadata (CC BY 4.0). orpha.net
Related codes
- E78.0 — Pure hypercholesterolemia
- E78.2 — Mixed hyperlipidemia
- E78.3 — Hyperchylomicronemia
- E78.4 — Other hyperlipidemia
- E78.5 — Hyperlipidemia, unspecified
- E78.6 — Lipoprotein deficiency
- E78.7 — Disorders of bile acid and cholesterol metabolism
- E78.8 — Other disorders of lipoprotein metabolism
- E78.9 — Disorder of lipoprotein metabolism, unspecified
Code hierarchy
ICD-10-CM data from CDC National Center for Health Statistics. For reference only. Disclaimer
Data accuracy: ICD-10-CM data from official public domain sources (CDC NCHS, CMS, NLM). For reference and coding assistance.
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