E78.6 Lipoprotein deficiency

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Lipoprotein deficiency

E78.6BillableFY 2026Chapter 4

Lipoprotein deficiency

Lipoprotein deficiency Abetalipoproteinemia; Depressed HDL cholesterol; High-density lipoprotein deficiency; Hypoalphalipoproteinemia; Hypobetalipoproteinemia (familial); Lecithin cholesterol acyltransferase deficiency; Tangier disease

Code classification

4Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88Metabolic disorders (E70-E88)
E78.6Current code

Related terminologies

ORPHA identifiers (rare diseases)

This ICD-10 code maps to the following rare disease(s) in the Orphanet nomenclature:

ORPHA CodeDisease Name
ORPHA:14Abetalipoproteinemia
ORPHA:181431Rare hypolipidemia
ORPHA:2388Choreoacanthocytosis
ORPHA:31150Tangier disease
ORPHA:425Apolipoprotein A-I deficiency
ORPHA:650LCAT deficiency
ORPHA:71Chylomicron retention disease
ORPHA:79292Fish-eye disease
ORPHA:79293Familial LCAT deficiency

Data from Orphadata (CC BY 4.0). orpha.net

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ICD-10-CM data from CDC National Center for Health Statistics. For reference only. Disclaimer

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